FH/Fumarase Rabbit pAb

• Background :

  Fumarase (FH) is an enzyme that catalyzes the reversible hydration/dehydration of fumarate to malate in the mitochondria. Fumarase deficiency is caused by a mutation in the fumarase gene in humans. Fumarase deficiency is one of the few known deficiencies of the Krebs cycle or tricarboxylic acid cycle, the main enzymatic pathway of cellular aerobic respiration.

• Description :

  Fumarase (FH) is an enzyme that catalyzes the reversible hydration/dehydration of fumarate to malate in the mitochondria. Fumarase deficiency is caused by a mutation in the fumarase gene in humans. Fumarase deficiency is one of the few known deficiencies of the Krebs cycle or tricarboxylic acid cycle, the main enzymatic pathway of cellular aerobic respiration.

• Product Name Alternative :

  Fumarase, fumarate hydratase, HLRCC, LRCC, MCL, MCUL1

• UniProt :

  P07954

• Swiss Prot :

  P07954

• Reactivity :

  Human, Rat, Mouse

• Immunogen :

  Recombinant Protein

• Clonality :

  Polyclonal

• Source :

  Rabbit

• Applications :

  WB, IF

• Concentration :

  1mg/mL

• Dilution :

  WB 1:1,000

• Buffer :

  PBS with 0.02% sodium azide and 50% glycerol pH 7.4. Store at -20°C. Avoid repeated freeze-thaw cycles.

• Molecular Weight :

  50kDa

• Storage Conditions :

  PBS with 0.02% sodium azide and 50% glycerol pH 7.4. Store at -20°C. Avoid repeated freeze-thaw cycles.

• Observed Molecular Weight :

  50kDa

• Fragment :

  IgG

• Other Product Names :

  Fumarase, fumarate hydratase, HLRCC, LRCC, MCL, MCUL1

• Gene ID (Human) :

  2271