HEM6 rabbit pAb

• Background :

  The protein encoded by this gene is the sixth enzyme of the heme biosynthetic pathway. The encoded enzyme is soluble and found in the intermembrane space of mitochondria. This enzyme catalyzes the stepwise oxidative decarboxylation of coproporphyrinogen III to protoporphyrinogen IX, a precursor of heme. Defects in this gene are a cause of hereditary coproporphyria (HCP) .[provided by RefSeq, Oct 2009]

• Description :

  The protein encoded by this gene is the sixth enzyme of the heme biosynthetic pathway. The encoded enzyme is soluble and found in the intermembrane space of mitochondria. This enzyme catalyzes the stepwise oxidative decarboxylation of coproporphyrinogen III to protoporphyrinogen IX, a precursor of heme. Defects in this gene are a cause of hereditary coproporphyria (HCP). [provided by RefSeq, Oct 2009],

• UniProt :

  P36551

• Swiss Prot :

  P36551

• Reactivity :

  Human; Mouse; Rat

• Immunogen :

  Synthesized peptide derived from human HEM6 AA range: 265-315

• Target :

  HEM6

• Clonality :

  Polyclonal

• Source :

  Rabbit

• Applications :

  WB

• Concentration :

  1 mg/ml

• Dilution :

  WB 1:500-2000

• Buffer :

  -20°C/1 year

• Storage Conditions :

  -20°C/1 year

• Fragment :

  IgG

• Subcellular Location :

  Mitochondrion intermembrane space.

• Gene ID (Human) :

  1371